Lysosomes and Lysosomal Storage Diseases

157 in the delivery room, and the normal newborn with a number of very pertinent sections about the situations in which the neonate finds himself in most serious trouble. The chapter on assessment of gestational age, for example, has both pictures and charts which will allow the physician to compare the physical examination in the patient with established standards. Pictures are of excellent quality and the discussions that accompany them are quite helpful. The same can be said of the photographs and the discussion in the chapter on physical examination. The chapter on infant nutrition is highly practical and helpful. It presents a balanced view of the proper nutrition of the infant, including the practical aspects of breast feeding. Neonatal emergencies are covered succinctly but clearly. Persistent fetal circulation, a potentially lethal problem, is well covered, as well as other respiratory problems such as apnea and respiratory distress. The chapter discussing caring for the family after a perinatal death is particularly helpful and should be read by both obstetricians and pediatricians who care for pregnant women and neonates. It is a sensitive and carefully thought-out discussion of a little-recognized aspect of pediatric care. The discussion on transport of the ill infant to a tertiary center and the most common urgent situations and their acute management are clearly and succinctly discussed. Surgical emergencies such as bowel obstruction, esophageal atresia, gastroschisis, and necrotizing enterocolitis are also presented. The second section is devoted to procedural techniques. It begins with information on obtaining the simulators developed at Indiana University, which allow the practice of procedures without jeopardizing real infants. The section on procedures is thorough and the drawings are helpful, but it should not be construed as sufficient to read this and then be able to perform these procedures without practice on simulators or as a part of pediatric or neonatology training. The section on procedures, as the other sections, would be helpful to pediatricians who have been trained to do these procedures but do not use them frequently. They will also be helpful to pediatric housestaff in training who are learning these procedures and need a textbook to which to refer. This book will be of value in the hospital emergency room, for referral by emergency room physicians faced with a gravely ill or apneic neonate perhaps awaiting transfer to a tertiary center. The appendix, which contains prototypes of orders and protocols used …